Keratosis Follicularis Spinulosa Decalvans Associated With Acne Keloidalis Nuchae And Tufted Hair Folliculitis

January 2008 in “ American Journal of Clinical Dermatology ”

Shahbaz A. Janjua, Nadia Iftikhar, Zrinjka Paštar, Gregory A. Hosler

keratosis follicularis spinulosa decalvans scarring alopecia keratosis pilaris acne keloidalis nuchae tufted hair folliculitis palmoplantar keratoderma KFSD scarring hair loss follicular keratosis keloid acne tufted folliculitis

Studysummary This case report further supports the association of keratosis follicularis spinulosa decalvans with acne keloidalis nuchae and tufted hair folliculitis.

Our plain-language summary. Not medical advice or a treatment recommendation. Consult a qualified healthcare professional before changing treatment. Full disclaimer

Keratosis follicularis spinulosa decalvans (KFSD) was a rare, X-linked disorder characterized by scarring alopecia of the scalp and eyebrows, often accompanied by widespread keratosis pilaris. The condition was sometimes associated with ocular abnormalities and palmoplantar keratoderma. This report documented a case of KFSD with acne keloidalis nuchae and tufted hair folliculitis, further supporting the association between these conditions. Previously, acne keloidalis nuchae had been described in only one other patient with KFSD, highlighting the rarity and complexity of these overlapping dermatological conditions.

View this study on link.springer.com →

Discuss this study in the Community →

Research cited in this study

4 / 4 results

research Keratosis Follicularis Spinulosa Decalvans And Acne Keloidalis Nuchae

37 citations , September 2005 in “Australasian Journal of Dermatology”

This case report describes a 27-year-old man with a unique association of keratosis follicularis spinulosa decalvans and acne keloidalis nuchae, successfully treated with oral isotretinoin.

research Clinical Findings, Cutaneous Pathology, and Response to Therapy in 21 Patients With Keratosis Pilaris Atrophicans

78 citations , April 1994 in “Archives of dermatology”

This study suggests genetic and clinical heterogeneity in keratosis pilaris atrophicans, with variations in inheritance patterns, severity, and response to treatment among 21 individuals observed.

research Keratosis Follicularis Spinulosa Decalvans: A Family Study of Seven Male Cases and Six Female Carriers

41 citations , January 1992 in “Journal of medical genetics”

This study described seven male patients and six female carriers of keratosis follicularis spinulosa decalvans, highlighting distinct dermatological and ophthalmic markers including follicular hyperkeratosis and corneal dystrophy.

research Keratosis Follicularis Spinulosa Decalvans

54 citations , January 1983 in “Archives of Dermatology”

This article presents two cases of keratosis follicularis spinulosa decalvans and reviews its features, highlighting characteristic progression from keratosis pilaris in infancy to cicatricial alopecia in childhood.