Keratosis Follicularis Spinulosa Decalvans in a Female

    Flavia Sequeira, Elizabeth Jayaseelan
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    TLDR A rare genetic skin condition usually affecting males was found in a 9-year-old girl.
    Keratosis follicularis spinulosa decalvans (KFSD) is a rare genetic condition characterized by widespread keratosis pilaris and progressive scarring alopecia, typically starting in infancy or early childhood with an X-linked inheritance pattern. It predominantly affects males, while females usually exhibit no symptoms or only mild forms. This document described a rare case of KFSD in a 9-year-old female child.
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