Keratosis Follicularis Spinulosa Decalvans: Case Report
August 2010
in “
Anais brasileiros de dermatologia/Anais Brasileiros de Dermatologia
”
![Image of study](/images/research/ea991564-75ee-4c5c-be5c-f1260e61c3bc/medium/36981.jpg)
TLDR A rare genetic disease caused severe, worsening hair loss from early childhood with poor treatment results.
Keratosis follicularis spinulosa decalvans is a rare genetic disease characterized by follicular hyperkeratosis and cicatricial alopecia, typically starting in early childhood and worsening during adolescence. The case reported involved a child with severe cicatricial alopecia from birth, which quickly progressed to widespread scalp alopecia, resulting in limited and disappointing treatment outcomes.