Congenital Atrichia Associated With Nevus Flammeus: A Rare Association

The document reported a rare case of a six-month-old infant with congenital atrichia, characterized by the absence of hair from birth, associated with nevus flammeus, a type of birthmark. The infant, born to consanguineous parents, exhibited complete hair loss on the occipital and temporal regions of the scalp, eyebrows, and eyelashes, with partial hair loss on the parietal and frontal regions. The diagnosis was confirmed through clinical examination and trichoscopy, which showed terminal hair without perifollicular abnormalities. The case was significant as it was the first reported instance of congenital atrichia with nevus flammeus, highlighting the need for further follow-up to monitor potential developments such as papular lesions or neurological issues.