Becker’s Nevus Syndrome in a Pediatric Female Patient
January 2016
in “
Case reports in pediatrics
”
TLDR A girl with Becker's nevus syndrome showed good improvement in breast development using spironolactone.
Becker's nevus syndrome, part of the epidermal nevus syndromes, was described with a phenotype including Becker's nevus, ipsilateral breast hypoplasia, and variable skeletal malformations. It was more frequent in males (5:1) but more relevant in females. Diagnosis was clinically based on the presence of the skin lesion, with no established numbered criteria. Treatment for breast hypoplasia using 50 mg/day of spironolactone, an antiandrogen medication, demonstrated adequate clinical response.