Becker Nevus Syndrome
June 2010
in “
Anais Brasileiros De Dermatologia
”
TLDR The document reports the first Brazilian case of a girl with Becker nevus syndrome, characterized by skin changes, breast underdevelopment, and scoliosis.
The document described the first reported case of Becker nevus syndrome in Brazilian literature, involving a 14-year-old girl with the condition. Becker's nevus is a skin hamartoma that presents with hyperpigmentation and hypertrichosis, and the syndrome can include other abnormalities such as breast hypoplasia and skeletal issues. The patient exhibited a hyperchromic macule with irregular borders and hypertrichosis on her right leg and scapular region, right breast hypogenesis, and scoliosis. Histopathology confirmed the diagnosis, and other tests were normal except for the scoliosis and breast hypotrophy. The syndrome, which is more common in males and often intensifies during adolescence, may be associated with increased androgen receptors, and spironolactone could potentially improve hypoplasia due to its antiandrogen effects. The syndrome is typically sporadic with few familial cases, and its genetic basis is not fully understood.
