Ichthyosis Linearis Circumflexa in a Child: Response to Narrowband UVB Therapy

December 2015 in “ Journal of Dermatological Case Reports ”

Ralfi Singer, Mehmet Sitki Copur, Ece Nur Yüksel, Emek Kocatürk, Selma Şengiz Erhan

ichthyosis linearis circumflexa narrowband UVB phototherapy Netherton syndrome emollients keratolytics systemic retinoids UVB therapy retinoids

TLDR Narrowband UVB therapy significantly improved a child's rare skin condition.

A 12-year-old boy with ichthyosis linearis circumflexa, a rare skin disorder, showed significant improvement after 30 sessions of narrowband UVB phototherapy. This treatment was well-tolerated and led to a five-month remission. The study suggested that narrowband UVB phototherapy could be an effective and safe treatment option for managing ichthyosis linearis circumflexa/Netherton syndrome, especially considering the side effects of topical therapies and the inconsistent results from systemic retinoids.

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