Circumscribed Juvenile Pityriasis Rubra Pilaris in a 5-Year-Old Girl Treated with Topical Keratolytic and Steroid
August 2018
in “
Journal of The American Academy of Dermatology
”
TLDR A 5-year-old girl with a rare skin disorder was effectively treated with skin creams instead of oral medication.
The document presents a case of a 5-year-old girl diagnosed with circumscribed juvenile pityriasis rubra pilaris (PRP), a rare papulosquamous disorder. The girl had a 2-week history of erythematous, follicular papules coalescing into plaques with whitish scales over her elbows and knees, along with palmoplantar keratoderma. Histopathologic examination confirmed the diagnosis of PRP. She was treated with a combination of topical keratolytic and steroid (betamethasone diproprionate + salicylic acid ointment), which led to complete resolution of lesions after 2 weeks. The conclusion of the case report emphasizes that, given the multiple adverse effects of the commonly used oral retinoid acitretin, patients with circumscribed juvenile PRP can be effectively treated with topical therapies such as keratolytics and steroids.
