Netherton's Syndrome And Ichthyosis Linearis Circumflexa

The document discussed a case of a 22-year-old woman with ichthyosis serpentina, bamboo hair, periodic hair loss, atopic eczema, pulmonary tuberculosis, and asthma, suggesting a variant of ichthyosis associated with trichorrhexis invaginata (bamboo hair). It noted that atopy was present in some cases but absent in others, indicating it was not a necessary component of the syndrome. The report also mentioned a 2-year-old sister showing broken hair shafts, highlighting a potential familial link.