Dermatopathia Pigmentosa Reticularis with Salzmann’s Nodular Degeneration of Cornea: A Rare Association
September 2015
in “
Nepalese journal of ophthalmology
”
TLDR An 11-year-old girl with a rare skin disorder also had cornea issues and dry eye, needing careful management.
An 11-year-old Indian girl with Dermatopathia pigmentosa reticularis (DPR), a rare autosomal dominant disorder characterized by generalized reticulate hyperpigmentation, noncicatricial alopecia, and onychodystrophy, was found to have Salzmann's nodular degeneration of the cornea and moderate dry eye. She received symptomatic treatment and was advised on disease management, including sun exposure avoidance. The case highlighted the importance of considering DPR in patients with similar symptoms and recommended a multidisciplinary approach for effective management.
