Hypotrichosis congenita of Marie Unna

The document described a case of a 54-year-old woman with hypotrichosis congenita, who was born with normal hair but experienced progressive hair loss, particularly during adolescence. Her scalp hair became sparse and formed a pattern similar to androgenetic alopecia of the Ludwig type, though it was asymmetrical. Additionally, her remaining hair was coarse, and she had almost no eyebrows or eyelashes, with sparse body hair. Her nails, teeth, and other ectodermal structures were normal.